Deficiency of which of the following enzymes is associated with von Gierke’s disease?

[Joyce]

#january2020usmle2k

Deficiency of which of the following enzymes is associated with von Gierke’s disease?

A- α-1,4-phosphorylase
B- Glucose-6-phosphatase
C- Hexosaminidase A
D- Phosphofructokinase-1

 

[Tiffany Wong]

A- α-1,4-phosphorylase