Several members of a family have an autosomal recessive disease characterized by intellectual deterioration, weakness, ataxia, seizures, and death at

[Kathryn]

#february2020mccqe1

Several members of a family have an autosomal recessive disease characterized by intellectual deterioration, weakness, ataxia, seizures, and death at a young age. Special studies demonstrate a deficiency of cytochrome C oxidase activity. Which of the following subcellular organelles is defective in affected members of this family?
(A) Golgi apparatus
(B) Lysosomes
(C) Mitochondria
(D) Ribosomes
(E) Smooth endoplasmic reticulum